non-Langerhans cell histiocytosis necrobiotic xanthogranuloma https://rarediseases.info.nih.gov/diseases/10951/necrobiotic-xanthogranuloma https://www.malacards.org/card/necrobiotic_xanthogranuloma EFO:1001376 MESH:D058252 MEDGEN:266158 ICD9:709.8 MONDO:0015537 icd11.foundation:2138563851 A cutaneous necrobiotic disorder characterized by firm, yellow plaques or nodules, often in a periorbital distribution. It is often accompanied by an elevated erythrocyte sedimentation rate; leukopenia; and monoclonal gammopathy (IgG-kappa type) and systemic involvement. UMLS:C1275339 SCTID:404164003 NXG Orphanet:158011 GARD:0010951