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    <!-- http://purl.obolibrary.org/obo/MONDO_0015584 -->

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        <rdfs:label>febrile infection-related epilepsy syndrome</rdfs:label>
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        <ns3:IAO_0000233 rdf:datatype="http://www.w3.org/2001/XMLSchema#anyURI">https://github.com/monarch-initiative/mondo/issues/5957</ns3:IAO_0000233>
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        <oboInOwl:hasExactSynonym>severe refractory status epilepticus owing to presumed encephalitis</oboInOwl:hasExactSynonym>
        <oboInOwl:hasDbXref>NANDO:1200600</oboInOwl:hasDbXref>
        <oboInOwl:hasExactSynonym>AERRPS</oboInOwl:hasExactSynonym>
        <oboInOwl:hasExactSynonym>acute encephalitis with refractory repetitive partial seizures</oboInOwl:hasExactSynonym>
        <oboInOwl:hasExactSynonym>acute non-herpetic encephalitis with severe refractory status epilepticus</oboInOwl:hasExactSynonym>
        <oboInOwl:id>MONDO:0015584</oboInOwl:id>
        <ns3:IAO_0000115>A rare, potentially fatal, epileptic encephalopathy characterized by explosive-onset of recurrent multifocal and bilateral tonic-clonic seizures following an unspecific febrile illness. The syndrome develops without a clear acute structural, toxic or metabolic cause, in a patient without previous epilepsy. FIRES is a subgroup of new-onset refractory status epilepticus (NORSE), and requires a preceding febrile infection as a mandatory feature.</ns3:IAO_0000115>
        <oboInOwl:hasExactSynonym>idiopathic catastrophic epileptic encephalopathy</oboInOwl:hasExactSynonym>
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        <oboInOwl:hasExactSynonym>FIRES</oboInOwl:hasExactSynonym>
        <oboInOwl:hasExactSynonym>DESC syndrome</oboInOwl:hasExactSynonym>
        <oboInOwl:hasExactSynonym>devastating epileptic encephalopathy in school-aged children</oboInOwl:hasExactSynonym>
        <oboInOwl:hasDbXref>MEDGEN:1381987</oboInOwl:hasDbXref>
        <oboInOwl:hasDbXref>Orphanet:163703</oboInOwl:hasDbXref>
        <oboInOwl:hasDbXref>GARD:0011005</oboInOwl:hasDbXref>
        <oboInOwl:hasDbXref>NANDO:2100249</oboInOwl:hasDbXref>
        <oboInOwl:hasExactSynonym>Febrile Infection-Related Epilepsy Syndrome (FIRES)</oboInOwl:hasExactSynonym>
        <oboInOwl:hasExactSynonym>fever-induced refractory epileptic encephalopathy in school-aged children</oboInOwl:hasExactSynonym>
        <oboInOwl:hasDbXref>SCTID:725413002</oboInOwl:hasDbXref>
        <oboInOwl:hasRelatedSynonym>status epilepticus owing to presumed encephalitis</oboInOwl:hasRelatedSynonym>
        <oboInOwl:hasDbXref>NORD:1889</oboInOwl:hasDbXref>
        <oboInOwl:hasDbXref>NANDO:2200903</oboInOwl:hasDbXref>
        <oboInOwl:hasDbXref>UMLS:C4049262</oboInOwl:hasDbXref>
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        <rdfs:label>childhood-onset epilepsy syndrome with developmental and/or epileptic encephalopathy</rdfs:label>
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