idiopathic pulmonary artery dilatation https://github.com/monarch-initiative/mondo/issues/6740 https://github.com/monarch-initiative/mondo/issues/6876 https://rarediseases.info.nih.gov/diseases/6757/idiopathic-dilatation-of-the-pulmonary-artery https://www.malacards.org/card/idiopathic_pulmonary_artery_dilatation MEDGEN:1842555 GARD:0006757 MONDO:0015664 Idiopathic pulmonary artery dilatation is a rare developmental defect during embryogenesis characterized by the dilatation of the main pulmonary artery, with or without dilatation of the right and left pulmonary artery branches, and not attributed to any other cardiac, pulmonary and/or arterial wall disease. It may present with exertional dyspnea, fatigue, cough, hemoptysis, palpitation and chest pain, but may also be asymptomatic. In serious cases, trachea constriction due to postural changes may lead to attacks of cyanosis with severe dyspnea. Sudden cardiac death has been reported in some cases. UMLS:C1384816 Orphanet:1676 idiopathic dilatation of the pulmonary artery congenital anomaly of the great arteries idiopathic disease