postlingual non-syndromic genetic hearing loss https://github.com/monarch-initiative/mondo/issues/551 Orphanet:216452 postlingual non-syndromic genetic deafness Postlingual non-syndromic genetic deafness is a rare, genetically highly heterogeneous otorhinolaryngologic disease, resulting from inner and/or middle ear or hearing nerve anomalies, typically characterized by progressive, bilateral, moderate to profound hearing loss (mean sensorineural hearing impairment equal to 40 dB or more for 500-, 1,000-, and 2,000-Hz frequency tones in the better ear) which occurs after the onset of speech development and is not associated with visible external ear abnormalities or any other medical problems. Language development is not initially significantly delayed. SCTID:764097002 MEDGEN:1641874 isolated postlingual genetic deafness GARD:0025070 MONDO:0016298 UMLS:C4706678 nonsyndromic genetic hearing loss