hypertrophic cardiomyopathy progressive sensorineural hearing loss-hypertrophic cardiomyopathy syndrome https://www.malacards.org/card/progressive_sensorineural_hearing_loss_hypertrophic_cardiomyopathy_syndrome Orphanet:228012 UMLS:C4304831 progressive neurosensory deafness-hypertrophic cardiomyopathy syndrome GARD:0017145 MEDGEN:930500 MONDO:0016424 progressive sensorineural deafness-hypertrophic cardiomyopathy syndrome Editor note: Orphanet xrefs OMIM:606346 which is DFNA22, check this progressive neurosensory hearing loss-hypertrophic cardiomyopathy syndrome Progressive sensorineural hearing loss - hypertrophic cardiomyopathy is an extremely rare disorder described in one family to date that is characterized by progressive, late onset, autosomal dominant sensorineural hearing loss, QT interval prolongation, and mild cardiac hypertrophy.