disease shares features of skin disorder pseudoxanthoma elasticum-like papillary dermal elastolysis https://www.malacards.org/card/pseudoxanthoma_elasticum_like_papillary_dermal_elastolysis Pseudoxanthoma elasticum-like papillary dermal elastolysis (PXE-PDE) is a rare, acquired, idiopathic dermal tissue disorder characterized by numerous, asymptomatic, 2-3 mm, yellowish, non-follicular papules that tend to converge into cobblestone-like plaques which are distributed symmetrically over the posterior neck, supraclavicular region, axillae, and sometimes abdomen. Unlike PXE, these skin lesions show select elimination (absence or marked loss) of elastic fibers in the papillary dermis and there is no systemic involvement. MONDO:0016448 MEDGEN:1638395 icd11.foundation:704601885 PXE-PDE PXE-like papillary dermal elastolysis UMLS:C4049455 Orphanet:228293 GARD:0020588 SCTID:764105002 pseudoxanthoma elasticum (inherited or acquired)