primary pulmonary lymphoma https://github.com/monarch-initiative/mondo/issues/8583 https://www.malacards.org/card/primary_pulmonary_lymphoma MEDGEN:903876 Orphanet:2420 Editor note: TODO check relationship to MONDO:0006387 primary pulmonary diffuse large B-cell lymphoma ; Reason of obsoletion: duplicate. This will be merged with MONDO:0003987 lung lymphoma icd11.foundation:1042489672 SCTID:718200007 MedDRA:10037418 Primary pulmonary lymphoma (PPL) is a rare lymphoma of the lung, defined as a clonal lymphoid proliferation affecting one or both lungs (parenchyma and/or bronchi) in a patient with no detectable extrapulmonary involvement at diagnosis or during the subsequent 3 months. PPL comprises low grade/indolent B cell PPL forms, the most frequent form represented by the marginal B-cell lymphoma of mucosa associated lymphoid tissue (MALT lymphoma) and other non-MALT low grade lymphomas; and more rarely high-grade B-cell PPL (including diffuse large B cell lymphoma) and lymphomatoid granulomatosis (LYG). 2025-04-01 MONDO:0016570 GARD:0018770 UMLS:C4273669 primary organ-specific lymphoma