nerve sheath neoplasm benign peripheral nerve sheath tumor neurofibroma https://rarediseases.info.nih.gov/diseases/7191/neurofibroma https://www.malacards.org/card/neurofibroma MESH:D009455 DOID:962 NCIT:C3272 ICDO:9540/0 SCTID:404029005 icd11.foundation:221014277 MONDO:0016755 MEDGEN:45058 neurofibroma (WHO grade I) UMLS:C0027830 ONCOTREE:NFIB An intraneural or extraneural neoplasm arising from nerve tissues and neural sheaths. It is composed of perineurial-like fibroblasts and Schwann cells. It usually presents as a localized cutaneous lesion and less often as a circumscribed peripheral nerve mass. Patients with neurofibromatosis type 1 present with multiple masses. Neurofibromas which arise from major nerves and plexiform neurofibromas are precursor lesions to malignant peripheral nerve sheath tumors. NFIB GARD:0007191 ICD9:215.9 Orphanet:252183 neurofibroma, benign MedDRA:10029267 neurofibroma