disease has location marginal zone B cell of spleen lymphoma indolent B-cell non-Hodgkin lymphoma marginal zone lymphoma https://www.malacards.org/card/marginal_zone_lymphoma lymphoma of marginal zone B cell A usually indolent mature B-cell lymphoma, arising from the marginal zone of lymphoid tissues. It is characterized by the presence of small to medium sized atypical lymphocytes. It comprises three entities, according to the anatomic sites involved: extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue, which affects extranodal sites (most often stomach, lung, skin, and ocular adnexa); nodal marginal zone B-cell lymphoma, which affects lymph nodes without evidence of extranodal disease; and splenic marginal zone B-cell lymphoma, which affects the spleen and splenic hilar lymph nodes, bone marrow, and often the peripheral blood. DOID:0050748 marginal zone B-cell lymphoma SCTID:447100004 MONDO:0017604 marginal zone B cell lymphoma ICDO:9699/3 ONCOTREE:MZL marginal zone lymphoma EFO:1000630 NCIT:C4341 GARD:0013237 MZBCL UMLS:C1367654 Orphanet:300912 MZL MEDGEN:277950 spleen neoplasm