disease has location mucinous adenocarcinoma colon mucinous adenocarcinoma appendix adenocarcinoma mucinous adenocarcinoma of the appendix https://www.malacards.org/card/mucinous_adenocarcinoma_of_the_appendix icd11.foundation:425095558 ONCOTREE:MAAP UMLS:C1706832 vermiform appendix mucinous adenocarcinoma Mucinous adenocarcinoma of the appendix is a very rare, slow growing, well-differentiated epithelial neoplasm of the appendix characterized by abundant mucin production. Clinically, it presents as acute appendicitis (with abdominal pain, fever, leukocytosis) or as pseudomyxoma peritonei (wide-spread presence of mucin within the peritoneal cavity), however some patients may be completely asymptomatic at the time of diagnosis. In many cases, a second gastrointestinal malignancy is present. MONDO:0018330 MEDGEN:317382 appendix mucinous adenocarcinoma NCIT:C43558 appendiceal mucinous adenocarcinoma GARD:0021629 Orphanet:391723 vermiform appendix