biliary tract disorder cirrhosis, familial isolated congenital hepatic fibrosis https://rarediseases.info.nih.gov/diseases/6168/congenital-hepatic-fibrosis https://www.malacards.org/card/isolated_congenital_hepatic_fibrosis MEDGEN:40449 congenital hepatic fibrosis nonsyndromic congenital hepatic fibrosis congenital fibrose liver NANDO:2100267 MONDO:0018840 isolated CHF SCTID:79607001 ICD9:777.8 NORD:1225 Congenital Hepatic Fibrosis UMLS:C0009714 NCIT:C97071 A congenital disorder usually inherited in an autosomal recessive pattern. It affects the hepatobiliary system and the kidneys. It is characterized by liver fibrosis, portal hypertension, and renal cysts. Orphanet:485426 NANDO:2200936 GARD:0021995 MESH:C562378