primary cutis verticis gyrata https://rarediseases.info.nih.gov/diseases/1643/cutis-verticis-gyrata https://www.malacards.org/card/primary_cutis_verticis_gyrata GARD:0001643 UMLS:C0263417 Orphanet:671 icd11.foundation:71926572 Cutis verticis gyrata (CVG) is a progressive cutaneous disorder predominantly affecting males and characterized by hypertrophy and thickening of the skin of the scalp forming convoluted furrows with deep, tender, and cerebriform cutaneous folds. Hair is usually normal in the furrows and sparse on the folds. CG can be isolated (essential CVG) or associated with other abnormalities such as intellectual deficit, epilepsy, cataract, blindness, and deafness (non essential CVG). MONDO:0019033 cutis verticis gyrata MEDGEN:78095 SCTID:51603000 ICD9:757.39 dermis disorder