primary lymphedema https://www.malacards.org/card/primary_lymphedema GARD:0018932 UMLS:C5576443 NANDO:2201031 NCIT:C48829 MONDO:0019175 primary lymphedema A congenital condition that results in swelling in the arms or legs, and can occur during adolescence or adulthood. Loss of motion and pain may also accompany the swelling. Protein-rich lymphatic fluid accumulates in tissues, engorging and enlarging vessels and often causing visible swelling, tenderness, and pain. Left untreated, the affected tissues may continue to swell, and can become hardened or fibrotic and susceptible to infection. Troncular lymphatic malformation icd11.foundation:794588197 Orphanet:77240 MEDGEN:1804666 lymphedema