atypical lichen myxedematosus localized lichen myxedematosus with monoclonal gammopathy or systemic symptoms https://www.malacards.org/card/localized_lichen_myxedematosus_with_monoclonal_gammopathy_or_systemic_symptoms UMLS:C5681466 MONDO:0019584 Localized lichen myxedematosus with monoclonal gammopathy or systemic symptoms is a form of atypical lichen myxedematosus, characterized by the appearance of several 2-4 mm erythematous waxy papules confined to a few sites that may be associated with either an immunoglobulin A (IgA) nephropathy in patients with acral persistent papular mucinosis; discrete papular lichen myxedematosus; a scleromyxedema-like involvement, with dysphagia, hoarseness, pulmonary involvement, and carpal tunnel syndrome; myositis without skin sclerosis; or paraproteinemia. Orphanet:90399 MEDGEN:1843442 GARD:0019143