immunotactoid or fibrillary glomerulopathy https://rarediseases.info.nih.gov/diseases/12741/immunotactoid-or-fibrillary-glomerulopathy https://www.malacards.org/card/immunotactoid_or_fibrillary_glomerulopathy UMLS:C5680195 Orphanet:91137 MEDGEN:1842578 A group of very rare glomerular diseases, composed of immunotactoid glomerulopathy (ITG) and non-amyloid fibrillary glomerulopathy (non-amyloid FGP), that are characterized by mesangial deposition of monoclonal microtubular or polyclonal fibrillar deposits. Both present clinically with nephrotic range proteinuria, hematuria and renal insufficiency leading to renal failure in many cases. ITG is more likely to manifest with underlying lymphoproliferative disease, hypocomplementemia, dysproteinemia, monoclonal gammopathy or occult cryoglobulinemia. Non-amyloid FGP is 10 times more frequent than ITG. Immunotactoid or fibrillary glomerulonephritis fibrillary glomerulonephritis and immunotactoid glomerulopathy MONDO:0019605 GARD:0012741 glomerular disorder obsolete secondary glomerular disease