diffuse large B-cell lymphoma intravascular large B-cell lymphoma https://www.malacards.org/card/intravascular_large_b_cell_lymphoma MedDRA:10069643 intravascular lymphomatosis angiotropic lymphoma intravascular B-cell lymphoma GARD:0019590 IVBCL Tappeiner-Pfleger disease ONCOTREE:IVBCL DOID:0081311 MEDGEN:90821 UMLS:C0334660 Orphanet:98839 Intravascular large B-cell lymphoma (IVLBCL) is a very rare form of diffuse large B-cell lymphoma characterized by the selective growth of lymphoma cells within the lumina of small blood vessels (especially the capillaries) that most often presents with a wide range of clinical manifestations (as potentially any tissue can be involved), with patients from Western countries more frequently manifesting with neurological and cutaneous symptoms while patients from Asian countries more frequently displaying hepatosplenomegaly and thrombocytopenia. IVLBCL is characterized by an absence of lymphadenopathy, an aggressive clinical course and a poor prognosis. MONDO:0020324 malignant angioendotheliomatosis angioendotheliomatosis proliferans systemisata ICDO:9712/3 intravascular large B-cell lymphoma icd11.foundation:952730197 ICD9:202.80 angiotropic large cell lymphoma SCTID:255102004 NCIT:C4342