aortic arch defects encircling double aortic arch https://www.malacards.org/card/encircling_double_aortic_arch Encircling double aortic arch is a very rare congenital anomaly of the great arteries characterized by the presence of two aortic arches (right and left) which encircle and compress the trachea and esophagus, resulting in various respiratory and gastrointestinal symptoms (e.g. harsh breathing, stridor, dyspnea, cyanotic and choking episodes, chronic cough, recurrent respiratory tract infections, dysphagia and reflux). Esophageal atresia and tracheoesophageal fistula have also been reported. It usually occurs isolated, but, on occasion, may be associated with other congenital heart anomalies and chromosomal aberations. MEDGEN:1641325 SCTID:764521002 Orphanet:99075 NANDO:2200290 MONDO:0020413 GARD:0019635 UMLS:C4706940