Ewing sarcoma/peripheral primitive neuroectodermal tumor extraskeletal Ewing sarcoma/peripheral primitive neuroectodermal tumor https://www.malacards.org/card/extraosseous_ewings_sarcoma_primitive_neuroepithelial_tumor MEDGEN:232170 A spectrum of malignant tumors arising from the soft tissues, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. Pain and the presence of a mass are the most common clinical symptoms. extraosseous Ewing's tumour extraosseous Ewing's tumor DOID:4985 extraosseous Ewings sarcoma-primitive neuroepithelial tumor NCIT:C27293 extraosseous Ewing's sarcoma/peripheral primitive neuroectodermal tumor MONDO:0021039 extraosseous Ewing sarcoma/peripheral primitive neuroectodermal tumour UMLS:C1333514 extraosseous Ewing's sarcoma/peripheral primitive neuroectodermal tumour extraosseous Ewing sarcoma/peripheral primitive neuroectodermal tumor EFO:1000250 extraskeletal Ewing sarcoma/peripheral primitive neuroectodermal tumor