disease has feature hypotropia mixed neuronal-glial tumor desmoplastic infantile astrocytoma https://rarediseases.info.nih.gov/diseases/9617/desmoplastic-infantile-astrocytoma NCIT:C9476 ICDO:9412/1 A WHO grade I large cystic tumor that occurs almost exclusively in infants, with a prominent desmoplastic stroma having a neuroepithelial population consisting mainly of neoplastic astrocytes. It involves the superficial cerebral cortex and leptomeninges, and often attaches to the dura. Although clinically it presents as large tumor, it generally has a good prognosis following surgical resection. (Adapted from WHO) MEDGEN:141595 ONCOTREE:DIA Desmoplastic infantile astrocytoma GARD:0009617 MONDO:0022963 Desmoplastic astrocytoma of infancy UMLS:C0457179 DIA