malignant exocrine pancreas neoplasm solid pseudopapillary neoplasm of the pancreas Frantz tumour GARD:0027975 Frantz tumor ONCOTREE:SPN MEDGEN:234800 UMLS:C1336030 solid pseudopapillary tumor of the pancreas solid pseudopapillary neoplasm of the pancreas MONDO:0044786 NCIT:C37212 solid pseudopapillary tumour of the pancreas A low-grade malignant neoplasm that arises from the exocrine pancreas. It is characterized by the presence of uniform cells that form solid and pseudopapillary patterns, cystic changes, and hemorrhage. Perineural invasion, vascular invasion, and invasion into surrounding tissues may be present. It usually presents as an encapsulated, solitary, and lobulated pancreatic mass. It is usually found incidentally during physical examination or it may present with abdominal discomfort and pain. It occurs predominantly in young women. Complete removal of the tumor is curative in the majority of cases.