patterned dystrophy of the retinal pigment epithelium butterfly-shaped pigment dystrophy https://github.com/monarch-initiative/mondo/issues/1819 https://www.malacards.org/card/butterfly_shaped_pigment_dystrophy icd11.foundation:1639469808 MEDGEN:1381271 butterfly-shaped pigmentary macular dystrophy butterfly-shaped pigment dystrophy MONDO:0100466 A patterned dystrophy of the retinal pigment epithelium characterized by abnormal accumulation of lipofuscin in a butterfly-shaped distribution at the retinal pigment epithelium level. Patients manifest with a slowly progressive loss of vision that often only becomes apparent in old age. UMLS:C4511237 butterfly-shaped pattern dystrophy GARD:0016890 SCTID:725590001 Orphanet:99001