Neuroectodermal Tumors, Primitive, Peripheral [Disease/Finding] Neuroectodermal Tumors, Primitive, Peripheral 1022217 C7608 Neuroectodermal Tumors, Primitive, Peripheral 253096008 254764001 Peripheral Primitive Neuroectodermal Tumors Neuroectodermal Neoplasm, Peripheral Primitive Peripheral Primitive Neuroectodermal Neoplasm A group of highly cellular primitive round cell neoplasms which occur extracranially in soft tissue and bone and are derived from embryonal neural crest cells. These tumors occur primarily in children and adolescents and share a number of characteristics with Ewing's Sarcoma (SARCOMA, EWING'S). They may arise from the chest wall, skin, orbit, kidney, and other structures and tend to be locally invasive or metastasize, although relatively benign forms may occur. Characteristic histologic features include a tendency to form Homer-Wright rosettes and to stain positively with neuron-specific enolase and vimentin. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2113; J Clin Oncol 1998 Mar;16(3):1150-7) Neuroectodermal Tumor, Peripheral Primitive D018241 Neuroectodermal Tumor, Peripheral M0027470 N0000003715 C0684337 Extracranial Primitive Neuroectodermal Tumor Primitive Neuroectodermal Tumor, Extracranial (pPNET) Peripheral Primitive Neuroectodermal Tumors Neuroectodermal Tumors, Primitive [Disease/Finding]